Additional file 1: Figure S1. Lung pathology of the ACDMPV pt 217.3. (A) Pulmonary artery branches show medial concentric hypertrophy. One artery shows microangiopathic changes with erythrocytes in vessel wall (H&E, 200x). (B) Hypertrophic arteries (arrowheads) in the bronchovascular bundles accompanied by thin-walled shunt vessels (“misaligned pulmonary veins”; arrows) (H&E, 200x). (C) Lower magnification demonstrating dilated lymphatic channels (*) and shunt vessels (arrows) (H&E, 100x).